Table 1

Motor phenomena scores in patients and controls

Motor phenomenaNarcolepsy with cataplexy, mean ± SDControls, mean ± SDP-value
Negative
    Head drop and falls
        Baseline0.31 ± 0.720.00 ± 0.000.017
        Trigger1.25 ± 0.840.04 ± 0.20<0.0005
    Ptosis and tongue protrusion
        Baseline0.78 ± 0.830.00 ± 0.00<0.0005
        Trigger1.66 ± 0.860.00 ± 0.00<0.0005
    Facial hypotonia
        Baseline0.73 ± 0.940.00 ± 0.00<0.0005
        Trigger1.42 ± 0.930.00 ± 0.00<0.0005
    Generalized hypotonia
        Baseline0.55 ± 0.900.00 ± 0.000.001
        Trigger0.88 ± 1.020.00 ± 0.00<0.0005
Positive
    Eyebrow raising
        Baseline0.29 ± 0.520.02 ± 0.100.013
        Trigger1.11 ± 0.810.44 ± 0.460.001
    Perioral and tongue movements
        Baseline0.55 ± 0.640.26 ± 0.410.047
        Trigger1.59 ± 0.590.74 ± 0.50<0.0005
    Facial grimaces
        Baseline0.22 ± 0.550.08 ± 0.190.404
        Trigger1.12 ± 0.680.50 ± 0.43<0.0005
    Head/trunk swaying
        Baseline0.42 ± 0.530.00 ± 0.00<0.0005
        Trigger1.29 ± 0.720.14 ± 0.34<0.0005
    Stereotyped motor behaviour
        Baseline0.22 ± 0.440.02 ± 0.100.024
        Trigger0.82 ± 0.800.30 ± 0.380.006
    Dyskinetic–dystonic movements
        Baseline0.13 ± 0.320.00 ± 0.000.041
        Trigger0.74 ± 0.710.12 ± 0.30<0.0005
Consistent patterns
    Neck extension viewing0.24 ± 0.430.00 ± 0.000.009
    Puppet-like behaviour0.13 ± 0.340.00 ± 0.000.064
Composite scores
    Composite negative
        Baseline2.37 ± 3.210.00 ± 0.00<0.0005
        Trigger5.21 ± 3.330.04 ± 0.20<0.0005
    Composite active
        Baseline1.83 ± 2.350.38 ± 0.460.001
        Trigger5.55 ± 2.691.80 ± 1.05<0.0005
Motor phenomenaNarcolepsy with cataplexy, mean ± SDControls, mean ± SDP-value
Negative
    Head drop and falls
        Baseline0.31 ± 0.720.00 ± 0.000.017
        Trigger1.25 ± 0.840.04 ± 0.20<0.0005
    Ptosis and tongue protrusion
        Baseline0.78 ± 0.830.00 ± 0.00<0.0005
        Trigger1.66 ± 0.860.00 ± 0.00<0.0005
    Facial hypotonia
        Baseline0.73 ± 0.940.00 ± 0.00<0.0005
        Trigger1.42 ± 0.930.00 ± 0.00<0.0005
    Generalized hypotonia
        Baseline0.55 ± 0.900.00 ± 0.000.001
        Trigger0.88 ± 1.020.00 ± 0.00<0.0005
Positive
    Eyebrow raising
        Baseline0.29 ± 0.520.02 ± 0.100.013
        Trigger1.11 ± 0.810.44 ± 0.460.001
    Perioral and tongue movements
        Baseline0.55 ± 0.640.26 ± 0.410.047
        Trigger1.59 ± 0.590.74 ± 0.50<0.0005
    Facial grimaces
        Baseline0.22 ± 0.550.08 ± 0.190.404
        Trigger1.12 ± 0.680.50 ± 0.43<0.0005
    Head/trunk swaying
        Baseline0.42 ± 0.530.00 ± 0.00<0.0005
        Trigger1.29 ± 0.720.14 ± 0.34<0.0005
    Stereotyped motor behaviour
        Baseline0.22 ± 0.440.02 ± 0.100.024
        Trigger0.82 ± 0.800.30 ± 0.380.006
    Dyskinetic–dystonic movements
        Baseline0.13 ± 0.320.00 ± 0.000.041
        Trigger0.74 ± 0.710.12 ± 0.30<0.0005
Consistent patterns
    Neck extension viewing0.24 ± 0.430.00 ± 0.000.009
    Puppet-like behaviour0.13 ± 0.340.00 ± 0.000.064
Composite scores
    Composite negative
        Baseline2.37 ± 3.210.00 ± 0.00<0.0005
        Trigger5.21 ± 3.330.04 ± 0.20<0.0005
    Composite active
        Baseline1.83 ± 2.350.38 ± 0.460.001
        Trigger5.55 ± 2.691.80 ± 1.05<0.0005
Table 1

Motor phenomena scores in patients and controls

Motor phenomenaNarcolepsy with cataplexy, mean ± SDControls, mean ± SDP-value
Negative
    Head drop and falls
        Baseline0.31 ± 0.720.00 ± 0.000.017
        Trigger1.25 ± 0.840.04 ± 0.20<0.0005
    Ptosis and tongue protrusion
        Baseline0.78 ± 0.830.00 ± 0.00<0.0005
        Trigger1.66 ± 0.860.00 ± 0.00<0.0005
    Facial hypotonia
        Baseline0.73 ± 0.940.00 ± 0.00<0.0005
        Trigger1.42 ± 0.930.00 ± 0.00<0.0005
    Generalized hypotonia
        Baseline0.55 ± 0.900.00 ± 0.000.001
        Trigger0.88 ± 1.020.00 ± 0.00<0.0005
Positive
    Eyebrow raising
        Baseline0.29 ± 0.520.02 ± 0.100.013
        Trigger1.11 ± 0.810.44 ± 0.460.001
    Perioral and tongue movements
        Baseline0.55 ± 0.640.26 ± 0.410.047
        Trigger1.59 ± 0.590.74 ± 0.50<0.0005
    Facial grimaces
        Baseline0.22 ± 0.550.08 ± 0.190.404
        Trigger1.12 ± 0.680.50 ± 0.43<0.0005
    Head/trunk swaying
        Baseline0.42 ± 0.530.00 ± 0.00<0.0005
        Trigger1.29 ± 0.720.14 ± 0.34<0.0005
    Stereotyped motor behaviour
        Baseline0.22 ± 0.440.02 ± 0.100.024
        Trigger0.82 ± 0.800.30 ± 0.380.006
    Dyskinetic–dystonic movements
        Baseline0.13 ± 0.320.00 ± 0.000.041
        Trigger0.74 ± 0.710.12 ± 0.30<0.0005
Consistent patterns
    Neck extension viewing0.24 ± 0.430.00 ± 0.000.009
    Puppet-like behaviour0.13 ± 0.340.00 ± 0.000.064
Composite scores
    Composite negative
        Baseline2.37 ± 3.210.00 ± 0.00<0.0005
        Trigger5.21 ± 3.330.04 ± 0.20<0.0005
    Composite active
        Baseline1.83 ± 2.350.38 ± 0.460.001
        Trigger5.55 ± 2.691.80 ± 1.05<0.0005
Motor phenomenaNarcolepsy with cataplexy, mean ± SDControls, mean ± SDP-value
Negative
    Head drop and falls
        Baseline0.31 ± 0.720.00 ± 0.000.017
        Trigger1.25 ± 0.840.04 ± 0.20<0.0005
    Ptosis and tongue protrusion
        Baseline0.78 ± 0.830.00 ± 0.00<0.0005
        Trigger1.66 ± 0.860.00 ± 0.00<0.0005
    Facial hypotonia
        Baseline0.73 ± 0.940.00 ± 0.00<0.0005
        Trigger1.42 ± 0.930.00 ± 0.00<0.0005
    Generalized hypotonia
        Baseline0.55 ± 0.900.00 ± 0.000.001
        Trigger0.88 ± 1.020.00 ± 0.00<0.0005
Positive
    Eyebrow raising
        Baseline0.29 ± 0.520.02 ± 0.100.013
        Trigger1.11 ± 0.810.44 ± 0.460.001
    Perioral and tongue movements
        Baseline0.55 ± 0.640.26 ± 0.410.047
        Trigger1.59 ± 0.590.74 ± 0.50<0.0005
    Facial grimaces
        Baseline0.22 ± 0.550.08 ± 0.190.404
        Trigger1.12 ± 0.680.50 ± 0.43<0.0005
    Head/trunk swaying
        Baseline0.42 ± 0.530.00 ± 0.00<0.0005
        Trigger1.29 ± 0.720.14 ± 0.34<0.0005
    Stereotyped motor behaviour
        Baseline0.22 ± 0.440.02 ± 0.100.024
        Trigger0.82 ± 0.800.30 ± 0.380.006
    Dyskinetic–dystonic movements
        Baseline0.13 ± 0.320.00 ± 0.000.041
        Trigger0.74 ± 0.710.12 ± 0.30<0.0005
Consistent patterns
    Neck extension viewing0.24 ± 0.430.00 ± 0.000.009
    Puppet-like behaviour0.13 ± 0.340.00 ± 0.000.064
Composite scores
    Composite negative
        Baseline2.37 ± 3.210.00 ± 0.00<0.0005
        Trigger5.21 ± 3.330.04 ± 0.20<0.0005
    Composite active
        Baseline1.83 ± 2.350.38 ± 0.460.001
        Trigger5.55 ± 2.691.80 ± 1.05<0.0005
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