Crude distribution of specific IKD and CAKUT subgroups in incident IKD or CAKUT patients starting KRT in 2019, using data from the subset of registries with 2012 ERA PRD data available.
| Characteristics . | n . | pmp (%) . |
|---|---|---|
| Inherited kidney diseases | ||
| ADPKD | 805 | 8.7 (67.3) |
| Other cystic diseases | 89 | 1.0 (7.4) |
| Other rare genetic conditions | 68 | 0.7 (5.7) |
| Genetic nephrotic syndrome | 67 | 0.7 (5.6) |
| Alport syndrome | 56 | 0.6 (4.7) |
| Genetic tubulointerstitial disease | 38 | 0.4 (3.2) |
| Tubulopathies | 28 | 0.3 (2.3) |
| Familial amyloidosis | 11 | 0.1 (0.9) |
| Thrombotic microangiopathy of (potentially) genetic origin | 11 | 0.1 (0.9) |
| Lysosomal storage disorders | 9 | 0.1 (0.8) |
| Phakomatoses | 8 | 0.1 (0.7) |
| Hereditary nephropathy (subtype unknown) | 6 | 0.1 (0.5) |
| Congenital anomalies of the kidneys and urinary tract | ||
| Kidney abnormality | 58 | 0.6 (31.8) |
| Congenital dysplasia/hypoplasia | 45 | 0.5 (24.7) |
| Other | 13 | 0.1 (7.1) |
| Urinary tract abnormality | 124 | 1.3 (68.0) |
| Primary reflux nephropathy—sporadic | 78 | 0.8 (42.9) |
| Congenital neurogenic bladder | 14 | 0.2 (7.7) |
| Congenital vesico-ureteric junction obstruction | 11 | 0.1 (6.0) |
| Posterior urethral valves | 10 | 0.1 (5.5) |
| Other | 11 | 0.1 (5.9) |
| Characteristics . | n . | pmp (%) . |
|---|---|---|
| Inherited kidney diseases | ||
| ADPKD | 805 | 8.7 (67.3) |
| Other cystic diseases | 89 | 1.0 (7.4) |
| Other rare genetic conditions | 68 | 0.7 (5.7) |
| Genetic nephrotic syndrome | 67 | 0.7 (5.6) |
| Alport syndrome | 56 | 0.6 (4.7) |
| Genetic tubulointerstitial disease | 38 | 0.4 (3.2) |
| Tubulopathies | 28 | 0.3 (2.3) |
| Familial amyloidosis | 11 | 0.1 (0.9) |
| Thrombotic microangiopathy of (potentially) genetic origin | 11 | 0.1 (0.9) |
| Lysosomal storage disorders | 9 | 0.1 (0.8) |
| Phakomatoses | 8 | 0.1 (0.7) |
| Hereditary nephropathy (subtype unknown) | 6 | 0.1 (0.5) |
| Congenital anomalies of the kidneys and urinary tract | ||
| Kidney abnormality | 58 | 0.6 (31.8) |
| Congenital dysplasia/hypoplasia | 45 | 0.5 (24.7) |
| Other | 13 | 0.1 (7.1) |
| Urinary tract abnormality | 124 | 1.3 (68.0) |
| Primary reflux nephropathy—sporadic | 78 | 0.8 (42.9) |
| Congenital neurogenic bladder | 14 | 0.2 (7.7) |
| Congenital vesico-ureteric junction obstruction | 11 | 0.1 (6.0) |
| Posterior urethral valves | 10 | 0.1 (5.5) |
| Other | 11 | 0.1 (5.9) |
Primary renal diseases included in the IKD and CAKUT groups can be found in Supplementary Table S2.
Crude distribution of specific IKD and CAKUT subgroups in incident IKD or CAKUT patients starting KRT in 2019, using data from the subset of registries with 2012 ERA PRD data available.
| Characteristics . | n . | pmp (%) . |
|---|---|---|
| Inherited kidney diseases | ||
| ADPKD | 805 | 8.7 (67.3) |
| Other cystic diseases | 89 | 1.0 (7.4) |
| Other rare genetic conditions | 68 | 0.7 (5.7) |
| Genetic nephrotic syndrome | 67 | 0.7 (5.6) |
| Alport syndrome | 56 | 0.6 (4.7) |
| Genetic tubulointerstitial disease | 38 | 0.4 (3.2) |
| Tubulopathies | 28 | 0.3 (2.3) |
| Familial amyloidosis | 11 | 0.1 (0.9) |
| Thrombotic microangiopathy of (potentially) genetic origin | 11 | 0.1 (0.9) |
| Lysosomal storage disorders | 9 | 0.1 (0.8) |
| Phakomatoses | 8 | 0.1 (0.7) |
| Hereditary nephropathy (subtype unknown) | 6 | 0.1 (0.5) |
| Congenital anomalies of the kidneys and urinary tract | ||
| Kidney abnormality | 58 | 0.6 (31.8) |
| Congenital dysplasia/hypoplasia | 45 | 0.5 (24.7) |
| Other | 13 | 0.1 (7.1) |
| Urinary tract abnormality | 124 | 1.3 (68.0) |
| Primary reflux nephropathy—sporadic | 78 | 0.8 (42.9) |
| Congenital neurogenic bladder | 14 | 0.2 (7.7) |
| Congenital vesico-ureteric junction obstruction | 11 | 0.1 (6.0) |
| Posterior urethral valves | 10 | 0.1 (5.5) |
| Other | 11 | 0.1 (5.9) |
| Characteristics . | n . | pmp (%) . |
|---|---|---|
| Inherited kidney diseases | ||
| ADPKD | 805 | 8.7 (67.3) |
| Other cystic diseases | 89 | 1.0 (7.4) |
| Other rare genetic conditions | 68 | 0.7 (5.7) |
| Genetic nephrotic syndrome | 67 | 0.7 (5.6) |
| Alport syndrome | 56 | 0.6 (4.7) |
| Genetic tubulointerstitial disease | 38 | 0.4 (3.2) |
| Tubulopathies | 28 | 0.3 (2.3) |
| Familial amyloidosis | 11 | 0.1 (0.9) |
| Thrombotic microangiopathy of (potentially) genetic origin | 11 | 0.1 (0.9) |
| Lysosomal storage disorders | 9 | 0.1 (0.8) |
| Phakomatoses | 8 | 0.1 (0.7) |
| Hereditary nephropathy (subtype unknown) | 6 | 0.1 (0.5) |
| Congenital anomalies of the kidneys and urinary tract | ||
| Kidney abnormality | 58 | 0.6 (31.8) |
| Congenital dysplasia/hypoplasia | 45 | 0.5 (24.7) |
| Other | 13 | 0.1 (7.1) |
| Urinary tract abnormality | 124 | 1.3 (68.0) |
| Primary reflux nephropathy—sporadic | 78 | 0.8 (42.9) |
| Congenital neurogenic bladder | 14 | 0.2 (7.7) |
| Congenital vesico-ureteric junction obstruction | 11 | 0.1 (6.0) |
| Posterior urethral valves | 10 | 0.1 (5.5) |
| Other | 11 | 0.1 (5.9) |
Primary renal diseases included in the IKD and CAKUT groups can be found in Supplementary Table S2.
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