| Diagnosis . | Female/male . | Age (years mean; min–max) . |
|---|---|---|
| JSLE (n = 8) | 6/2 | 12 (7–17) |
| JDM (n = 9) | 2/7 | 9 (4–15) |
| Interferonopathy (n = 7) | 5/2 | 10 (3–15) |
| COPA (n = 3) | 3/0 | 8 (3–15) |
| AGS (n = 2) | 0/2 | 8 (5–10) |
| SAVI (n = 2) | 2/0 | 15 (14–15) |
| PF (n = 7) | 3/4 | 5 (2–8) |
| JIA (n = 8) | 6/2 | 7 (1–18) |
| Diagnosis . | Female/male . | Age (years mean; min–max) . |
|---|---|---|
| JSLE (n = 8) | 6/2 | 12 (7–17) |
| JDM (n = 9) | 2/7 | 9 (4–15) |
| Interferonopathy (n = 7) | 5/2 | 10 (3–15) |
| COPA (n = 3) | 3/0 | 8 (3–15) |
| AGS (n = 2) | 0/2 | 8 (5–10) |
| SAVI (n = 2) | 2/0 | 15 (14–15) |
| PF (n = 7) | 3/4 | 5 (2–8) |
| JIA (n = 8) | 6/2 | 7 (1–18) |
Abbreviations: AGS: Aicardi–Goutières syndrome; COPA: coatomer protein complex subunit alpha; JDM: juvenile dermatomyositis; JIA: juvenile idiopathic arthritis; JSLE: juvenile systemic lupus erythematosus; PF: periodic fevers; SAVI: STING (stimulator of interferon genes) associated vasculopathy with onset in infancy.
| Diagnosis . | Female/male . | Age (years mean; min–max) . |
|---|---|---|
| JSLE (n = 8) | 6/2 | 12 (7–17) |
| JDM (n = 9) | 2/7 | 9 (4–15) |
| Interferonopathy (n = 7) | 5/2 | 10 (3–15) |
| COPA (n = 3) | 3/0 | 8 (3–15) |
| AGS (n = 2) | 0/2 | 8 (5–10) |
| SAVI (n = 2) | 2/0 | 15 (14–15) |
| PF (n = 7) | 3/4 | 5 (2–8) |
| JIA (n = 8) | 6/2 | 7 (1–18) |
| Diagnosis . | Female/male . | Age (years mean; min–max) . |
|---|---|---|
| JSLE (n = 8) | 6/2 | 12 (7–17) |
| JDM (n = 9) | 2/7 | 9 (4–15) |
| Interferonopathy (n = 7) | 5/2 | 10 (3–15) |
| COPA (n = 3) | 3/0 | 8 (3–15) |
| AGS (n = 2) | 0/2 | 8 (5–10) |
| SAVI (n = 2) | 2/0 | 15 (14–15) |
| PF (n = 7) | 3/4 | 5 (2–8) |
| JIA (n = 8) | 6/2 | 7 (1–18) |
Abbreviations: AGS: Aicardi–Goutières syndrome; COPA: coatomer protein complex subunit alpha; JDM: juvenile dermatomyositis; JIA: juvenile idiopathic arthritis; JSLE: juvenile systemic lupus erythematosus; PF: periodic fevers; SAVI: STING (stimulator of interferon genes) associated vasculopathy with onset in infancy.
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