Table 1:

Patient baseline characteristics

VariableASO-R (n = 20)HTTS (n = 23)Nikaidoh (n = 21)Rastelli (n = 43)P-values
Male gender, n (%)13 (65)18 (78.3)11 (52.4)28 (65.1)0.4
Body weight (kg), median (IQR)7.6 (5.4–9.4)8 (6–10.3)9.2 (7.2–13.9)10.5 (7.5–18.1)<0.05
Age at surgery (years), median (IQR)0.7 (0.3–1)0.7 (0.5–1.6)0.8 (0.5–3.4)1.8 (0.6–6.7)<0.01
BSA (m², Boyd formula), median (IQR)0.4 (0.3–0.4)0.4 (0.3–0.5)0.5 (0.4–0.6)0.5 (0.4–0.8)0.1
Follow-up (years), median (IQR)2.1 (1–5.5)0.7 (0.1–4.5)5.8 (0.3–10.8)5.9 (0.5–14.8)0.1
l-TGA, n (%)7 (35)5 (21.7)2 (9.5)8 (18.6)0.3
Preterm birth, n (%)0 (0)4 (17.4)1 (4.8)0 (0)0.01
Genetic disorder, n (%)1 (5)1 (4.3)1 (4.8)2 (4.7)0.9
Situs inversus, n (%)0 (0)2 (8.7)1 (4.8)6 (14)0.3
Right aortic arch, n (%)1 (5)2 (8.7)1 (4.8)10 (23.3)0.1
Interrupted IVC, n (%)0 (0)0 (0)1 (4.8)1 (2.3)0.6
Echocardiographic characteristics
Level of LVOTO/PV stenosis
 Supravalvular, n (%)1 (5)0 (0)0 (0)0 (0)0.2
 Valvular, n (%)3 (15)2 (8.7)0 (0)4 (9.3)0.6
 Infundibular, n (%)8 (40)3 (13)0 (0)2 (4.7)<0.01
 Multilevel, n (%)8 (40)18 (78.3)15 (71.4)27 (62.7)0.04
Bicuspid PV, n (%)6 (30)7 (30.4)7 (33.3)7 (16.3)0.2
Pulmonary atresia, n (%)0 (0)0 (0)6 (28.6)10 (23.3)<0.01
PV Z-Score, median (IQR)–1.2 (–2.1 to 0.6)–3.1 (–4.2 to –2)–4.3 (–4.7 to –3)–3.6 (–5 to –2.4)<0.01
AoV Z-Score, median (IQR)3.9 (2.6–5.4)3.7 (2.5–6.3)4.2 (2.7–5.3)4.8 (3–7.2)0.5
LVOT peak gradient (mmHg), median (IQR)60 (41.5–80)70 (61.5–85)70 (61–84)75 (66–81)0.1
RVOT peak gradient (mmHg), median (IQR)3.5 (3–6)4 (3–5)4 (3–6)6 (4–7.5)0.1
VariableASO-R (n = 20)HTTS (n = 23)Nikaidoh (n = 21)Rastelli (n = 43)P-values
Male gender, n (%)13 (65)18 (78.3)11 (52.4)28 (65.1)0.4
Body weight (kg), median (IQR)7.6 (5.4–9.4)8 (6–10.3)9.2 (7.2–13.9)10.5 (7.5–18.1)<0.05
Age at surgery (years), median (IQR)0.7 (0.3–1)0.7 (0.5–1.6)0.8 (0.5–3.4)1.8 (0.6–6.7)<0.01
BSA (m², Boyd formula), median (IQR)0.4 (0.3–0.4)0.4 (0.3–0.5)0.5 (0.4–0.6)0.5 (0.4–0.8)0.1
Follow-up (years), median (IQR)2.1 (1–5.5)0.7 (0.1–4.5)5.8 (0.3–10.8)5.9 (0.5–14.8)0.1
l-TGA, n (%)7 (35)5 (21.7)2 (9.5)8 (18.6)0.3
Preterm birth, n (%)0 (0)4 (17.4)1 (4.8)0 (0)0.01
Genetic disorder, n (%)1 (5)1 (4.3)1 (4.8)2 (4.7)0.9
Situs inversus, n (%)0 (0)2 (8.7)1 (4.8)6 (14)0.3
Right aortic arch, n (%)1 (5)2 (8.7)1 (4.8)10 (23.3)0.1
Interrupted IVC, n (%)0 (0)0 (0)1 (4.8)1 (2.3)0.6
Echocardiographic characteristics
Level of LVOTO/PV stenosis
 Supravalvular, n (%)1 (5)0 (0)0 (0)0 (0)0.2
 Valvular, n (%)3 (15)2 (8.7)0 (0)4 (9.3)0.6
 Infundibular, n (%)8 (40)3 (13)0 (0)2 (4.7)<0.01
 Multilevel, n (%)8 (40)18 (78.3)15 (71.4)27 (62.7)0.04
Bicuspid PV, n (%)6 (30)7 (30.4)7 (33.3)7 (16.3)0.2
Pulmonary atresia, n (%)0 (0)0 (0)6 (28.6)10 (23.3)<0.01
PV Z-Score, median (IQR)–1.2 (–2.1 to 0.6)–3.1 (–4.2 to –2)–4.3 (–4.7 to –3)–3.6 (–5 to –2.4)<0.01
AoV Z-Score, median (IQR)3.9 (2.6–5.4)3.7 (2.5–6.3)4.2 (2.7–5.3)4.8 (3–7.2)0.5
LVOT peak gradient (mmHg), median (IQR)60 (41.5–80)70 (61.5–85)70 (61–84)75 (66–81)0.1
RVOT peak gradient (mmHg), median (IQR)3.5 (3–6)4 (3–5)4 (3–6)6 (4–7.5)0.1

AoV: aortic valve; ASO-R: arterial switch operation with resection of LVOTO; BSA: body surface area; HTTS: half-turned truncal switch; IQR: interquartile range; IVC: inferior vena cava; l-TGA: levo-transposition of the great arteries; LVOT: left ventricular outflow tract; LVOTO: left ventricular outflow tract obstruction; PV: pulmonary valve; RVOT: right ventricular outflow tract.

Significant P-values in bold.

Table 1:

Patient baseline characteristics

VariableASO-R (n = 20)HTTS (n = 23)Nikaidoh (n = 21)Rastelli (n = 43)P-values
Male gender, n (%)13 (65)18 (78.3)11 (52.4)28 (65.1)0.4
Body weight (kg), median (IQR)7.6 (5.4–9.4)8 (6–10.3)9.2 (7.2–13.9)10.5 (7.5–18.1)<0.05
Age at surgery (years), median (IQR)0.7 (0.3–1)0.7 (0.5–1.6)0.8 (0.5–3.4)1.8 (0.6–6.7)<0.01
BSA (m², Boyd formula), median (IQR)0.4 (0.3–0.4)0.4 (0.3–0.5)0.5 (0.4–0.6)0.5 (0.4–0.8)0.1
Follow-up (years), median (IQR)2.1 (1–5.5)0.7 (0.1–4.5)5.8 (0.3–10.8)5.9 (0.5–14.8)0.1
l-TGA, n (%)7 (35)5 (21.7)2 (9.5)8 (18.6)0.3
Preterm birth, n (%)0 (0)4 (17.4)1 (4.8)0 (0)0.01
Genetic disorder, n (%)1 (5)1 (4.3)1 (4.8)2 (4.7)0.9
Situs inversus, n (%)0 (0)2 (8.7)1 (4.8)6 (14)0.3
Right aortic arch, n (%)1 (5)2 (8.7)1 (4.8)10 (23.3)0.1
Interrupted IVC, n (%)0 (0)0 (0)1 (4.8)1 (2.3)0.6
Echocardiographic characteristics
Level of LVOTO/PV stenosis
 Supravalvular, n (%)1 (5)0 (0)0 (0)0 (0)0.2
 Valvular, n (%)3 (15)2 (8.7)0 (0)4 (9.3)0.6
 Infundibular, n (%)8 (40)3 (13)0 (0)2 (4.7)<0.01
 Multilevel, n (%)8 (40)18 (78.3)15 (71.4)27 (62.7)0.04
Bicuspid PV, n (%)6 (30)7 (30.4)7 (33.3)7 (16.3)0.2
Pulmonary atresia, n (%)0 (0)0 (0)6 (28.6)10 (23.3)<0.01
PV Z-Score, median (IQR)–1.2 (–2.1 to 0.6)–3.1 (–4.2 to –2)–4.3 (–4.7 to –3)–3.6 (–5 to –2.4)<0.01
AoV Z-Score, median (IQR)3.9 (2.6–5.4)3.7 (2.5–6.3)4.2 (2.7–5.3)4.8 (3–7.2)0.5
LVOT peak gradient (mmHg), median (IQR)60 (41.5–80)70 (61.5–85)70 (61–84)75 (66–81)0.1
RVOT peak gradient (mmHg), median (IQR)3.5 (3–6)4 (3–5)4 (3–6)6 (4–7.5)0.1
VariableASO-R (n = 20)HTTS (n = 23)Nikaidoh (n = 21)Rastelli (n = 43)P-values
Male gender, n (%)13 (65)18 (78.3)11 (52.4)28 (65.1)0.4
Body weight (kg), median (IQR)7.6 (5.4–9.4)8 (6–10.3)9.2 (7.2–13.9)10.5 (7.5–18.1)<0.05
Age at surgery (years), median (IQR)0.7 (0.3–1)0.7 (0.5–1.6)0.8 (0.5–3.4)1.8 (0.6–6.7)<0.01
BSA (m², Boyd formula), median (IQR)0.4 (0.3–0.4)0.4 (0.3–0.5)0.5 (0.4–0.6)0.5 (0.4–0.8)0.1
Follow-up (years), median (IQR)2.1 (1–5.5)0.7 (0.1–4.5)5.8 (0.3–10.8)5.9 (0.5–14.8)0.1
l-TGA, n (%)7 (35)5 (21.7)2 (9.5)8 (18.6)0.3
Preterm birth, n (%)0 (0)4 (17.4)1 (4.8)0 (0)0.01
Genetic disorder, n (%)1 (5)1 (4.3)1 (4.8)2 (4.7)0.9
Situs inversus, n (%)0 (0)2 (8.7)1 (4.8)6 (14)0.3
Right aortic arch, n (%)1 (5)2 (8.7)1 (4.8)10 (23.3)0.1
Interrupted IVC, n (%)0 (0)0 (0)1 (4.8)1 (2.3)0.6
Echocardiographic characteristics
Level of LVOTO/PV stenosis
 Supravalvular, n (%)1 (5)0 (0)0 (0)0 (0)0.2
 Valvular, n (%)3 (15)2 (8.7)0 (0)4 (9.3)0.6
 Infundibular, n (%)8 (40)3 (13)0 (0)2 (4.7)<0.01
 Multilevel, n (%)8 (40)18 (78.3)15 (71.4)27 (62.7)0.04
Bicuspid PV, n (%)6 (30)7 (30.4)7 (33.3)7 (16.3)0.2
Pulmonary atresia, n (%)0 (0)0 (0)6 (28.6)10 (23.3)<0.01
PV Z-Score, median (IQR)–1.2 (–2.1 to 0.6)–3.1 (–4.2 to –2)–4.3 (–4.7 to –3)–3.6 (–5 to –2.4)<0.01
AoV Z-Score, median (IQR)3.9 (2.6–5.4)3.7 (2.5–6.3)4.2 (2.7–5.3)4.8 (3–7.2)0.5
LVOT peak gradient (mmHg), median (IQR)60 (41.5–80)70 (61.5–85)70 (61–84)75 (66–81)0.1
RVOT peak gradient (mmHg), median (IQR)3.5 (3–6)4 (3–5)4 (3–6)6 (4–7.5)0.1

AoV: aortic valve; ASO-R: arterial switch operation with resection of LVOTO; BSA: body surface area; HTTS: half-turned truncal switch; IQR: interquartile range; IVC: inferior vena cava; l-TGA: levo-transposition of the great arteries; LVOT: left ventricular outflow tract; LVOTO: left ventricular outflow tract obstruction; PV: pulmonary valve; RVOT: right ventricular outflow tract.

Significant P-values in bold.

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