| Characteristic . | Anti-SAE + DM, n = 49 . |
|---|---|
| Skin manifestations, yes | 95.9 (47/49) |
| Erythema of the eyelids | 71.4 (35/49) |
| Periorbital oedema | 44.9 (22/49) |
| Gottron’s sign or papules | 77.5 (38/49) |
| Periungual erythema | 77.5 (38/49) |
| Erythema of the upper back (shawl sign) | 57.1 (28/49) |
| Erythema of the upper trunk (V sign) | 77.5 (38/49) |
| Lateral hip erythema (holster sign) | 34.7 (17/49) |
| Panniculitis | 8.2 (4/49) |
| Poikiloderma | 12.2 (6/49) |
| Alopecia | 8.2 (4/49) |
| Calcinosis | 10.2 (5/49) |
| Necrosis | 12.2 (6/49) |
| Cutaneous or mucosal ulceration | 18.4 (9/49) |
| Only skin disease at onset, (n = 15)a | 86.7 (13/15) |
| RP | 14.3 (7/49) |
| Characteristic . | Anti-SAE + DM, n = 49 . |
|---|---|
| Skin manifestations, yes | 95.9 (47/49) |
| Erythema of the eyelids | 71.4 (35/49) |
| Periorbital oedema | 44.9 (22/49) |
| Gottron’s sign or papules | 77.5 (38/49) |
| Periungual erythema | 77.5 (38/49) |
| Erythema of the upper back (shawl sign) | 57.1 (28/49) |
| Erythema of the upper trunk (V sign) | 77.5 (38/49) |
| Lateral hip erythema (holster sign) | 34.7 (17/49) |
| Panniculitis | 8.2 (4/49) |
| Poikiloderma | 12.2 (6/49) |
| Alopecia | 8.2 (4/49) |
| Calcinosis | 10.2 (5/49) |
| Necrosis | 12.2 (6/49) |
| Cutaneous or mucosal ulceration | 18.4 (9/49) |
| Only skin disease at onset, (n = 15)a | 86.7 (13/15) |
| RP | 14.3 (7/49) |
Quantitative variables are reported as median and interquartile range (IQR). Qualitative variables are reported as a percentage of the total of the available data. SAE: small ubiquitin like modifier activating enzyme.
Indicates the number of patients for whom data was available.
| Characteristic . | Anti-SAE + DM, n = 49 . |
|---|---|
| Skin manifestations, yes | 95.9 (47/49) |
| Erythema of the eyelids | 71.4 (35/49) |
| Periorbital oedema | 44.9 (22/49) |
| Gottron’s sign or papules | 77.5 (38/49) |
| Periungual erythema | 77.5 (38/49) |
| Erythema of the upper back (shawl sign) | 57.1 (28/49) |
| Erythema of the upper trunk (V sign) | 77.5 (38/49) |
| Lateral hip erythema (holster sign) | 34.7 (17/49) |
| Panniculitis | 8.2 (4/49) |
| Poikiloderma | 12.2 (6/49) |
| Alopecia | 8.2 (4/49) |
| Calcinosis | 10.2 (5/49) |
| Necrosis | 12.2 (6/49) |
| Cutaneous or mucosal ulceration | 18.4 (9/49) |
| Only skin disease at onset, (n = 15)a | 86.7 (13/15) |
| RP | 14.3 (7/49) |
| Characteristic . | Anti-SAE + DM, n = 49 . |
|---|---|
| Skin manifestations, yes | 95.9 (47/49) |
| Erythema of the eyelids | 71.4 (35/49) |
| Periorbital oedema | 44.9 (22/49) |
| Gottron’s sign or papules | 77.5 (38/49) |
| Periungual erythema | 77.5 (38/49) |
| Erythema of the upper back (shawl sign) | 57.1 (28/49) |
| Erythema of the upper trunk (V sign) | 77.5 (38/49) |
| Lateral hip erythema (holster sign) | 34.7 (17/49) |
| Panniculitis | 8.2 (4/49) |
| Poikiloderma | 12.2 (6/49) |
| Alopecia | 8.2 (4/49) |
| Calcinosis | 10.2 (5/49) |
| Necrosis | 12.2 (6/49) |
| Cutaneous or mucosal ulceration | 18.4 (9/49) |
| Only skin disease at onset, (n = 15)a | 86.7 (13/15) |
| RP | 14.3 (7/49) |
Quantitative variables are reported as median and interquartile range (IQR). Qualitative variables are reported as a percentage of the total of the available data. SAE: small ubiquitin like modifier activating enzyme.
Indicates the number of patients for whom data was available.
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