| CALM-phenotype . | All carriers . | Any cardiac events . | MAE . |
|---|---|---|---|
| (n = 140)a . | (n = 103)b,c . | (n = 77)c,d . | |
| LQTS | 74 (53) | 47 (64) | 36 (49) |
| CPVT | 36 (26) | 33 (92) | 20 (56) |
| IVF | 7 (5) | 5 (71) | 5 (71) |
| LQTS/CPVT overlap | 10 (7) | 7 (70) | 6 (60) |
| UD | 11 (8) | 11 (100) | 10 (91) |
| Atypical | 2 (1) | - | - |
| CALM-phenotype . | All carriers . | Any cardiac events . | MAE . |
|---|---|---|---|
| (n = 140)a . | (n = 103)b,c . | (n = 77)c,d . | |
| LQTS | 74 (53) | 47 (64) | 36 (49) |
| CPVT | 36 (26) | 33 (92) | 20 (56) |
| IVF | 7 (5) | 5 (71) | 5 (71) |
| LQTS/CPVT overlap | 10 (7) | 7 (70) | 6 (60) |
| UD | 11 (8) | 11 (100) | 10 (91) |
| Atypical | 2 (1) | - | - |
Data are numbers and (%) of subjects.
LQTS, long QT syndrome; CPVT, catecholaminergic polymorphic ventricular tachycardia; IVF, idiopathic ventricular fibrillation; MAE, major arrhythmic events; UD, uncertain diagnosis.
Percentage out of all 140 CALM patients.
Arrhythmic syncope, ACA, SCD, and appropriate ICD shocks.
Percentage in the corresponding phenotype group.
ACA, SCD, and appropriate ICD shocks.
| CALM-phenotype . | All carriers . | Any cardiac events . | MAE . |
|---|---|---|---|
| (n = 140)a . | (n = 103)b,c . | (n = 77)c,d . | |
| LQTS | 74 (53) | 47 (64) | 36 (49) |
| CPVT | 36 (26) | 33 (92) | 20 (56) |
| IVF | 7 (5) | 5 (71) | 5 (71) |
| LQTS/CPVT overlap | 10 (7) | 7 (70) | 6 (60) |
| UD | 11 (8) | 11 (100) | 10 (91) |
| Atypical | 2 (1) | - | - |
| CALM-phenotype . | All carriers . | Any cardiac events . | MAE . |
|---|---|---|---|
| (n = 140)a . | (n = 103)b,c . | (n = 77)c,d . | |
| LQTS | 74 (53) | 47 (64) | 36 (49) |
| CPVT | 36 (26) | 33 (92) | 20 (56) |
| IVF | 7 (5) | 5 (71) | 5 (71) |
| LQTS/CPVT overlap | 10 (7) | 7 (70) | 6 (60) |
| UD | 11 (8) | 11 (100) | 10 (91) |
| Atypical | 2 (1) | - | - |
Data are numbers and (%) of subjects.
LQTS, long QT syndrome; CPVT, catecholaminergic polymorphic ventricular tachycardia; IVF, idiopathic ventricular fibrillation; MAE, major arrhythmic events; UD, uncertain diagnosis.
Percentage out of all 140 CALM patients.
Arrhythmic syncope, ACA, SCD, and appropriate ICD shocks.
Percentage in the corresponding phenotype group.
ACA, SCD, and appropriate ICD shocks.
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