LV-DCM pts number (sex) . | Further diagnoses . | BW (kg) . | Age (mo.) at ePAB . | HR initial/min . | TAPSE (mm) . | LV-EDD (mm) (z-score) . | LV-EF (%) initial . | Ross-functional class (I–IV) . | Initial Th. E, NE, M, Levo CPAP/CV tc rASD . |
---|---|---|---|---|---|---|---|---|---|
1. (f) | LV-NC, MR I-II consanguine | 6.1 | 6 | 165 | 15 | 43 (+6.7) | 18 | IV | E, NE, M, Levo CPAP tc rASD |
2. (f) | LV-NC, MRI CRP rASD | 4.9 | 3 | 170 | 13 | 40 (+6,5) | 19 | IV | E, NE, M, Levo CV |
3. (m) | LV-NC,-Barth synd. PFO | 3.5 | 1.5 | 158 | 11 | 32 (+5.1) | 15 | IV | E, M, L |
LV-DCM pts number (sex) . | Further diagnoses . | BW (kg) . | Age (mo.) at ePAB . | HR initial/min . | TAPSE (mm) . | LV-EDD (mm) (z-score) . | LV-EF (%) initial . | Ross-functional class (I–IV) . | Initial Th. E, NE, M, Levo CPAP/CV tc rASD . |
---|---|---|---|---|---|---|---|---|---|
1. (f) | LV-NC, MR I-II consanguine | 6.1 | 6 | 165 | 15 | 43 (+6.7) | 18 | IV | E, NE, M, Levo CPAP tc rASD |
2. (f) | LV-NC, MRI CRP rASD | 4.9 | 3 | 170 | 13 | 40 (+6,5) | 19 | IV | E, NE, M, Levo CV |
3. (m) | LV-NC,-Barth synd. PFO | 3.5 | 1.5 | 158 | 11 | 32 (+5.1) | 15 | IV | E, M, L |
Abbreviations: ASA, acetyl-salicylic-acid; B, bisoprolol; Barth-Syndrome; BW, body weight; CV, controlled ventilation; CRP, cardiopulmonary resuscitation; DCM, dilated cardiomyopathy; E, epinephrine; EDD, enddiastolic diameter; EF, ejection fraction; ePAB, endo-pulmonary artery banding; f, female, HR, heart rate; L, lisinopril; Levo, levosimendan; LV, left ventricle; LV-NC, left ventricular non-compaction; m, male; M, milrinone; mo., months; MR, mitral regurgitation; NC, non-compaction; NE, norepinephrine; pts, patients; PFO, patent foramen ovale; rASD, restrictive atrial septum defect; S, spironolactone; TAPSE, tricuspid annular plane systolic excursion; tc, transcatheter.
LV-DCM pts number (sex) . | Further diagnoses . | BW (kg) . | Age (mo.) at ePAB . | HR initial/min . | TAPSE (mm) . | LV-EDD (mm) (z-score) . | LV-EF (%) initial . | Ross-functional class (I–IV) . | Initial Th. E, NE, M, Levo CPAP/CV tc rASD . |
---|---|---|---|---|---|---|---|---|---|
1. (f) | LV-NC, MR I-II consanguine | 6.1 | 6 | 165 | 15 | 43 (+6.7) | 18 | IV | E, NE, M, Levo CPAP tc rASD |
2. (f) | LV-NC, MRI CRP rASD | 4.9 | 3 | 170 | 13 | 40 (+6,5) | 19 | IV | E, NE, M, Levo CV |
3. (m) | LV-NC,-Barth synd. PFO | 3.5 | 1.5 | 158 | 11 | 32 (+5.1) | 15 | IV | E, M, L |
LV-DCM pts number (sex) . | Further diagnoses . | BW (kg) . | Age (mo.) at ePAB . | HR initial/min . | TAPSE (mm) . | LV-EDD (mm) (z-score) . | LV-EF (%) initial . | Ross-functional class (I–IV) . | Initial Th. E, NE, M, Levo CPAP/CV tc rASD . |
---|---|---|---|---|---|---|---|---|---|
1. (f) | LV-NC, MR I-II consanguine | 6.1 | 6 | 165 | 15 | 43 (+6.7) | 18 | IV | E, NE, M, Levo CPAP tc rASD |
2. (f) | LV-NC, MRI CRP rASD | 4.9 | 3 | 170 | 13 | 40 (+6,5) | 19 | IV | E, NE, M, Levo CV |
3. (m) | LV-NC,-Barth synd. PFO | 3.5 | 1.5 | 158 | 11 | 32 (+5.1) | 15 | IV | E, M, L |
Abbreviations: ASA, acetyl-salicylic-acid; B, bisoprolol; Barth-Syndrome; BW, body weight; CV, controlled ventilation; CRP, cardiopulmonary resuscitation; DCM, dilated cardiomyopathy; E, epinephrine; EDD, enddiastolic diameter; EF, ejection fraction; ePAB, endo-pulmonary artery banding; f, female, HR, heart rate; L, lisinopril; Levo, levosimendan; LV, left ventricle; LV-NC, left ventricular non-compaction; m, male; M, milrinone; mo., months; MR, mitral regurgitation; NC, non-compaction; NE, norepinephrine; pts, patients; PFO, patent foramen ovale; rASD, restrictive atrial septum defect; S, spironolactone; TAPSE, tricuspid annular plane systolic excursion; tc, transcatheter.
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