Table 4:

Risk factors for mortality after birth

Univariable model
Multivariable model
HR95% CIP-valueHR95% CIP-value
Morphology
 Right isomerism0.350.39–5.090.59
 Common AVV0.460.17–1.240.13
 Dextorcardia0.490.17–1.420.19
 Dominant right ventricle1.410.41–5.120.59
Pulmonary flow
 Restrictive2.810.90–8.740.083.231.02–10.20.05
 Balanced0.030.01–6.190.20
 Excessive0.890.29–2.750.83
Pulmonary venous return
 TAPVC1.550.56–4.260.40
 Extracardiac TAPVC0.560.36–3.050.92
 Obstructive TAPVC0.500.14–2.600.51
Systemic venous return
 Azygos continuation1.180.41–3.410.75
 Bilateral SVC0.860.31–2.350.76
AVV regurgitation
 Greater than mild AVVR3.061.11–8.480.033.571.27–10.00.02
Univariable model
Multivariable model
HR95% CIP-valueHR95% CIP-value
Morphology
 Right isomerism0.350.39–5.090.59
 Common AVV0.460.17–1.240.13
 Dextorcardia0.490.17–1.420.19
 Dominant right ventricle1.410.41–5.120.59
Pulmonary flow
 Restrictive2.810.90–8.740.083.231.02–10.20.05
 Balanced0.030.01–6.190.20
 Excessive0.890.29–2.750.83
Pulmonary venous return
 TAPVC1.550.56–4.260.40
 Extracardiac TAPVC0.560.36–3.050.92
 Obstructive TAPVC0.500.14–2.600.51
Systemic venous return
 Azygos continuation1.180.41–3.410.75
 Bilateral SVC0.860.31–2.350.76
AVV regurgitation
 Greater than mild AVVR3.061.11–8.480.033.571.27–10.00.02

AVV: atrioventricular valve; AVVR: atrioventricular valve regurgitation; HR: hazard ratio; SVC: superior vena cava; TAPVC: total anomalous pulmonary venous connection.

Table 4:

Risk factors for mortality after birth

Univariable model
Multivariable model
HR95% CIP-valueHR95% CIP-value
Morphology
 Right isomerism0.350.39–5.090.59
 Common AVV0.460.17–1.240.13
 Dextorcardia0.490.17–1.420.19
 Dominant right ventricle1.410.41–5.120.59
Pulmonary flow
 Restrictive2.810.90–8.740.083.231.02–10.20.05
 Balanced0.030.01–6.190.20
 Excessive0.890.29–2.750.83
Pulmonary venous return
 TAPVC1.550.56–4.260.40
 Extracardiac TAPVC0.560.36–3.050.92
 Obstructive TAPVC0.500.14–2.600.51
Systemic venous return
 Azygos continuation1.180.41–3.410.75
 Bilateral SVC0.860.31–2.350.76
AVV regurgitation
 Greater than mild AVVR3.061.11–8.480.033.571.27–10.00.02
Univariable model
Multivariable model
HR95% CIP-valueHR95% CIP-value
Morphology
 Right isomerism0.350.39–5.090.59
 Common AVV0.460.17–1.240.13
 Dextorcardia0.490.17–1.420.19
 Dominant right ventricle1.410.41–5.120.59
Pulmonary flow
 Restrictive2.810.90–8.740.083.231.02–10.20.05
 Balanced0.030.01–6.190.20
 Excessive0.890.29–2.750.83
Pulmonary venous return
 TAPVC1.550.56–4.260.40
 Extracardiac TAPVC0.560.36–3.050.92
 Obstructive TAPVC0.500.14–2.600.51
Systemic venous return
 Azygos continuation1.180.41–3.410.75
 Bilateral SVC0.860.31–2.350.76
AVV regurgitation
 Greater than mild AVVR3.061.11–8.480.033.571.27–10.00.02

AVV: atrioventricular valve; AVVR: atrioventricular valve regurgitation; HR: hazard ratio; SVC: superior vena cava; TAPVC: total anomalous pulmonary venous connection.

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