Table 1:

Patient characteristics and outcomes

Patient no.YearsSexAge at repairWeight (kg)Concomitant anomaliesPrior surgeryConcomitant repair with L-PAPVC repairReoperationsStatus
11980M299 days7.6NoneNoneNoneNoneAlive
21992F60 days3.6CoA; PDA; VSDNoneCoA repair; PDA ligation; VSD closureNoneAlive
31994M99 days5.2Hypoplastic RV; PDA; tricuspid atresia; VSD; hypoplastic left lungNonePA banding1. PV stenosis relief
2. MBTS
3. BCPC and RPA patch augmentation
4. Take-down of BCPC and rerouting of LPA to SVC
Alive
41996F1.2 years8.8PA sling; TOFMBTS 9 months earlierPA sling repair; VSD closureRVOT resection and 19 mm aortic homograft in RVOT to function with the native valveAlive
51998M4.8 years15.5R-PAPVCNoneR-PAPVC repairNoneAlive
61999M4.4 years16.0NoneNoneNoneNoneAlive
72000M17.1 years40.3ASD; Ehlers–Danlos syndromeASD repair 6 years earlierNoneNoneLate death
82000M3.6 years13.3ASDNoneASD closureNoneAlive
92001M12.2 years38.0ASDNoneASD closureNoneAlive
102001F4.1 years14.8CoA; PDANoneCoA repair; PDA ligationNoneAlive
112001M25 days3.5ASD; VSDNoneASD closureNoneAlive
122002F1.4 years10.5ASD; cor triatriatum; pulmonary valve stenosis; R-PAPVCNoneASD closure; cor triatriatum repair; R-PAPVC repairNoneAlive
132007M5 days2.6ASD; CoA; PDA; VSDNoneASD closure; CoA repair; PDA ligation; VSD closure; PA bandingPA band tightening and plication of left hemi-diaphragmAlive
142011F4.3 years16.8Bicuspid aortic valve; CoA; PDA; ASDCoA repair; PDA ligation 4 years earlierASD closureNoneAlive
152011F112 days5.1TOF; R-PAPVCNoneTOF repair; R-PAPVC repair1. Warden procedure
2. RVOT resection
Alive
Patient no.YearsSexAge at repairWeight (kg)Concomitant anomaliesPrior surgeryConcomitant repair with L-PAPVC repairReoperationsStatus
11980M299 days7.6NoneNoneNoneNoneAlive
21992F60 days3.6CoA; PDA; VSDNoneCoA repair; PDA ligation; VSD closureNoneAlive
31994M99 days5.2Hypoplastic RV; PDA; tricuspid atresia; VSD; hypoplastic left lungNonePA banding1. PV stenosis relief
2. MBTS
3. BCPC and RPA patch augmentation
4. Take-down of BCPC and rerouting of LPA to SVC
Alive
41996F1.2 years8.8PA sling; TOFMBTS 9 months earlierPA sling repair; VSD closureRVOT resection and 19 mm aortic homograft in RVOT to function with the native valveAlive
51998M4.8 years15.5R-PAPVCNoneR-PAPVC repairNoneAlive
61999M4.4 years16.0NoneNoneNoneNoneAlive
72000M17.1 years40.3ASD; Ehlers–Danlos syndromeASD repair 6 years earlierNoneNoneLate death
82000M3.6 years13.3ASDNoneASD closureNoneAlive
92001M12.2 years38.0ASDNoneASD closureNoneAlive
102001F4.1 years14.8CoA; PDANoneCoA repair; PDA ligationNoneAlive
112001M25 days3.5ASD; VSDNoneASD closureNoneAlive
122002F1.4 years10.5ASD; cor triatriatum; pulmonary valve stenosis; R-PAPVCNoneASD closure; cor triatriatum repair; R-PAPVC repairNoneAlive
132007M5 days2.6ASD; CoA; PDA; VSDNoneASD closure; CoA repair; PDA ligation; VSD closure; PA bandingPA band tightening and plication of left hemi-diaphragmAlive
142011F4.3 years16.8Bicuspid aortic valve; CoA; PDA; ASDCoA repair; PDA ligation 4 years earlierASD closureNoneAlive
152011F112 days5.1TOF; R-PAPVCNoneTOF repair; R-PAPVC repair1. Warden procedure
2. RVOT resection
Alive

ASD: atrial septal defect; BCPC: bidirectional cavopulmonary connection; CoA: coarctation of aorta; LA: left atrium; LPA: left pulmonary artery; MBTS: modified Blalock–Taussig shunt; PA: pulmonary artery; PAPVC: partially anomalous pulmonary venous connection; PDA: patent ductus arteriosus; PV: pulmonary vein; RA: right atrium; RPA: right pulmonary artery; RV: right ventricle; RVOT: right ventricular outflow tract; SVC: superior vena cava; TOF: tetralogy of Fallot; VSD: ventricular septal defect.

Table 1:

Patient characteristics and outcomes

Patient no.YearsSexAge at repairWeight (kg)Concomitant anomaliesPrior surgeryConcomitant repair with L-PAPVC repairReoperationsStatus
11980M299 days7.6NoneNoneNoneNoneAlive
21992F60 days3.6CoA; PDA; VSDNoneCoA repair; PDA ligation; VSD closureNoneAlive
31994M99 days5.2Hypoplastic RV; PDA; tricuspid atresia; VSD; hypoplastic left lungNonePA banding1. PV stenosis relief
2. MBTS
3. BCPC and RPA patch augmentation
4. Take-down of BCPC and rerouting of LPA to SVC
Alive
41996F1.2 years8.8PA sling; TOFMBTS 9 months earlierPA sling repair; VSD closureRVOT resection and 19 mm aortic homograft in RVOT to function with the native valveAlive
51998M4.8 years15.5R-PAPVCNoneR-PAPVC repairNoneAlive
61999M4.4 years16.0NoneNoneNoneNoneAlive
72000M17.1 years40.3ASD; Ehlers–Danlos syndromeASD repair 6 years earlierNoneNoneLate death
82000M3.6 years13.3ASDNoneASD closureNoneAlive
92001M12.2 years38.0ASDNoneASD closureNoneAlive
102001F4.1 years14.8CoA; PDANoneCoA repair; PDA ligationNoneAlive
112001M25 days3.5ASD; VSDNoneASD closureNoneAlive
122002F1.4 years10.5ASD; cor triatriatum; pulmonary valve stenosis; R-PAPVCNoneASD closure; cor triatriatum repair; R-PAPVC repairNoneAlive
132007M5 days2.6ASD; CoA; PDA; VSDNoneASD closure; CoA repair; PDA ligation; VSD closure; PA bandingPA band tightening and plication of left hemi-diaphragmAlive
142011F4.3 years16.8Bicuspid aortic valve; CoA; PDA; ASDCoA repair; PDA ligation 4 years earlierASD closureNoneAlive
152011F112 days5.1TOF; R-PAPVCNoneTOF repair; R-PAPVC repair1. Warden procedure
2. RVOT resection
Alive
Patient no.YearsSexAge at repairWeight (kg)Concomitant anomaliesPrior surgeryConcomitant repair with L-PAPVC repairReoperationsStatus
11980M299 days7.6NoneNoneNoneNoneAlive
21992F60 days3.6CoA; PDA; VSDNoneCoA repair; PDA ligation; VSD closureNoneAlive
31994M99 days5.2Hypoplastic RV; PDA; tricuspid atresia; VSD; hypoplastic left lungNonePA banding1. PV stenosis relief
2. MBTS
3. BCPC and RPA patch augmentation
4. Take-down of BCPC and rerouting of LPA to SVC
Alive
41996F1.2 years8.8PA sling; TOFMBTS 9 months earlierPA sling repair; VSD closureRVOT resection and 19 mm aortic homograft in RVOT to function with the native valveAlive
51998M4.8 years15.5R-PAPVCNoneR-PAPVC repairNoneAlive
61999M4.4 years16.0NoneNoneNoneNoneAlive
72000M17.1 years40.3ASD; Ehlers–Danlos syndromeASD repair 6 years earlierNoneNoneLate death
82000M3.6 years13.3ASDNoneASD closureNoneAlive
92001M12.2 years38.0ASDNoneASD closureNoneAlive
102001F4.1 years14.8CoA; PDANoneCoA repair; PDA ligationNoneAlive
112001M25 days3.5ASD; VSDNoneASD closureNoneAlive
122002F1.4 years10.5ASD; cor triatriatum; pulmonary valve stenosis; R-PAPVCNoneASD closure; cor triatriatum repair; R-PAPVC repairNoneAlive
132007M5 days2.6ASD; CoA; PDA; VSDNoneASD closure; CoA repair; PDA ligation; VSD closure; PA bandingPA band tightening and plication of left hemi-diaphragmAlive
142011F4.3 years16.8Bicuspid aortic valve; CoA; PDA; ASDCoA repair; PDA ligation 4 years earlierASD closureNoneAlive
152011F112 days5.1TOF; R-PAPVCNoneTOF repair; R-PAPVC repair1. Warden procedure
2. RVOT resection
Alive

ASD: atrial septal defect; BCPC: bidirectional cavopulmonary connection; CoA: coarctation of aorta; LA: left atrium; LPA: left pulmonary artery; MBTS: modified Blalock–Taussig shunt; PA: pulmonary artery; PAPVC: partially anomalous pulmonary venous connection; PDA: patent ductus arteriosus; PV: pulmonary vein; RA: right atrium; RPA: right pulmonary artery; RV: right ventricle; RVOT: right ventricular outflow tract; SVC: superior vena cava; TOF: tetralogy of Fallot; VSD: ventricular septal defect.

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